欧美精品日韩在线视频-久久视频精彩在线观看-精品少妇人妻一区二区黑-欧美日韩中文字幕人妻-丁香九月婷婷综合在线-久久久亚洲熟妇熟女一区-久久久久免费看片-日本中文字幕人妻少妇在线-女同久久另类99精品国产,欧美 另类 自拍偷拍,中文字幕人妻系列懂色av,久久久亚洲精品男人的天堂

首頁(yè) > 抗體 > 一抗 > 其它 > Pax-6 Monoclonal Antibody
Pax-6 Monoclonal Antibody
商品貨號(hào)： PLA004980
適 應(yīng) 性： 人
WB ELISA FCM
￥600元
規(guī)格：
在線咨詢
MSDS
說(shuō)明書
商品描述
  • 發(fā)貨日期： 7
  • 基因名稱： PAX6
  • 蛋白名稱： Paired box protein Pax-6
  • Human_gene_id： 5080
  • Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=5080
  • Human_swiss_prot_no： P26367
  • Human_swiss_link： http://www.uniprot.org/uniprotkb/P26367/entry
  • Mouse_swiss_prot_no： P63015
  • Mouse_swiss_link： http://www.uniprot.org/uniprot/P63015
  • 特異性： Pax-6 Monoclonal Antibody detects endogenous levels of Pax-6 protein.
  • 組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來(lái)源： Monoclonal, Mouse
  • 稀釋： WB 1:500 - 1:2000. Flow cytometry: 1:200 - 1:400. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝： Affinity purification
  • 儲(chǔ)存： -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說(shuō)明書： 1
  • Msds： MSDS_Antibody.pdf
  • 其他名稱： PAX6; AN2; Paired box protein Pax-6; Aniridia type II protein; Oculorhombin
  • 信號(hào)通路： Maturity onset diabetes of the young;
  • 功能： developmental stage:Expressed in the developing eye and brain.,disease:Defects in PAX6 are a cause of autosomal dominant keratitis [MIM:148190]. It is an eye disorder characterized by corneal opacification and vascularization, and by foveal hypoplasia.,disease:Defects in PAX6 are a cause of bilateral optic nerve hypoplasia [MIM:165550]; also known as bilateral optic nerve aplasia. Inheritance is autosomal dominant.,disease:Defects in PAX6 are a cause of coloboma of optic nerve [MIM:120430].,disease:Defects in PAX6 are a cause of ectopia pupillae [MIM:129750]. It is a congenital eye malformation in which the pupils are displaced from their normal central position.,disease:Defects in PAX6 are a cause of foveal hypoplasia [MIM:136520]. Foveal hypoplasia can be isolated or associated with presenile cataract. Inheritance is autosomal dominant.,disease:Defects in PAX6 are a cause of Gillespie syndrome [MIM:206700]; also called aniridia cerebellar ataxia and mental deficiency. Gillespie syndrome is a rare condition consisting of partial rudimentary iris, cerebellar impairment of the ability to perform smoothly coordinated voluntary movements, and mental retardation. It is not yet clear whether the disorder has an autosomal recessive or dominant inheritance.,disease:Defects in PAX6 are a cause of ocular coloboma [MIM:120200]; also known as uveoretinal coloboma or coloboma of iris, choroid and retina. Ocular colobomas are a set of malformations resulting from abnormal morphogenesis of the optic cup and stalk, and the fusion of the fetal fissure (optic fissure). Severe colobomatous malformations may cause as much as 10% of the childhood blindness. The clinical presentation of ocular coloboma is variable. Some individuals may present with minimal defects in the anterior iris leaf without other ocular defects. More complex malformations create a combination of iris, uveoretinal and/or optic nerve defects without or with microphthalmia or even anophthalmia.,disease:Defects in PAX6 are a cause of Peters anomaly [MIM:604229]. Peters anomaly consists of a central corneal leukoma, absence of the posterior corneal stroma and Descemet membrane, and a variable degree of iris and lenticular attachments to the central aspect of the posterior cornea.,disease:Defects in PAX6 are the cause of aniridia type II (AN2) [MIM:106210]. AN2 is a bilateral panocular disorder characterized by complete or partial absence of the iris, absence of the fovea and malformations of the lens and anterior chamber. Severe age-related corneal degeneration is a frequent complication which contributes to a poor visual prognostis in aniridia. About one third of the cases are sporadic, and two thirds are familial, with autosomal dominant inheritance and high penetrance. Nearly one third of sporadic AN patients develop Wilms tumor in association with genitourinary anomalies and mental retardation (WAGR syndrome) as a consequence of heterozygous (sub)microscopic deletions of chromosome 11p13.,function:Transcription factor with important functions in the development of the eye, nose, central nervous system and pancreas. Required for the differentiation of pancreatic islet alpha cells (By similarity). Competes with PAX4 in binding to a common element in the glucagon, insulin and somatostatin promoters. Regulates specification of the ventral neuron subtypes by establishing the correct progenitor domains (By similarity). Isoform 5a appears to function as a molecular switch that specifies target genes.,similarity:Belongs to the paired homeobox family.,similarity:Contains 1 homeobox DNA-binding domain.,similarity:Contains 1 paired domain.,subunit:Interacts with MAF and MAFB.,tissue specificity:Fetal eye, brain, spinal cord and olfactory epithelium. Isoform 5a is less abundant than the PAX6 shorter form.,
  • 相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
  • 細(xì)胞定位： Nucleus .; [Isoform 1]: Nucleus .; [Isoform 5a]: Nucleus .
  • 組織表達(dá)： [Isoform 1]: Expressed in lymphoblasts. ; [Isoform 5a]: Weakly expressed in lymphoblasts.
  • 科研貨號(hào)： PLA004980
Pax-6 Monoclonal Antibody
Catalog No PLA004980
Product information
  • 發(fā)貨日期： 7
  • 基因名稱： PAX6
  • 蛋白名稱： Paired box protein Pax-6
  • Human_gene_id： 5080
  • Human_gene_link： http://www.ncbi.nlm.nih.gov/sites/entrez?db=gene&term=5080
  • Human_swiss_prot_no： P26367
  • Human_swiss_link： http://www.uniprot.org/uniprotkb/P26367/entry
  • Mouse_swiss_prot_no： P63015
  • Mouse_swiss_link： http://www.uniprot.org/uniprot/P63015
  • 特異性： Pax-6 Monoclonal Antibody detects endogenous levels of Pax-6 protein.
  • 組成： Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide.
  • 來(lái)源： Monoclonal, Mouse
  • 稀釋： WB 1:500 - 1:2000. Flow cytometry: 1:200 - 1:400. ELISA: 1:10000. Not yet tested in other applications.
  • 純化工藝： Affinity purification
  • 儲(chǔ)存： -15°C to -25°C/1 year(Do not lower than -25°C)
  • 說(shuō)明書： 1
  • Msds： MSDS_Antibody.pdf
  • 其他名稱： PAX6; AN2; Paired box protein Pax-6; Aniridia type II protein; Oculorhombin
  • 信號(hào)通路： Maturity onset diabetes of the young;
  • 功能： developmental stage:Expressed in the developing eye and brain.,disease:Defects in PAX6 are a cause of autosomal dominant keratitis [MIM:148190]. It is an eye disorder characterized by corneal opacification and vascularization, and by foveal hypoplasia.,disease:Defects in PAX6 are a cause of bilateral optic nerve hypoplasia [MIM:165550]; also known as bilateral optic nerve aplasia. Inheritance is autosomal dominant.,disease:Defects in PAX6 are a cause of coloboma of optic nerve [MIM:120430].,disease:Defects in PAX6 are a cause of ectopia pupillae [MIM:129750]. It is a congenital eye malformation in which the pupils are displaced from their normal central position.,disease:Defects in PAX6 are a cause of foveal hypoplasia [MIM:136520]. Foveal hypoplasia can be isolated or associated with presenile cataract. Inheritance is autosomal dominant.,disease:Defects in PAX6 are a cause of Gillespie syndrome [MIM:206700]; also called aniridia cerebellar ataxia and mental deficiency. Gillespie syndrome is a rare condition consisting of partial rudimentary iris, cerebellar impairment of the ability to perform smoothly coordinated voluntary movements, and mental retardation. It is not yet clear whether the disorder has an autosomal recessive or dominant inheritance.,disease:Defects in PAX6 are a cause of ocular coloboma [MIM:120200]; also known as uveoretinal coloboma or coloboma of iris, choroid and retina. Ocular colobomas are a set of malformations resulting from abnormal morphogenesis of the optic cup and stalk, and the fusion of the fetal fissure (optic fissure). Severe colobomatous malformations may cause as much as 10% of the childhood blindness. The clinical presentation of ocular coloboma is variable. Some individuals may present with minimal defects in the anterior iris leaf without other ocular defects. More complex malformations create a combination of iris, uveoretinal and/or optic nerve defects without or with microphthalmia or even anophthalmia.,disease:Defects in PAX6 are a cause of Peters anomaly [MIM:604229]. Peters anomaly consists of a central corneal leukoma, absence of the posterior corneal stroma and Descemet membrane, and a variable degree of iris and lenticular attachments to the central aspect of the posterior cornea.,disease:Defects in PAX6 are the cause of aniridia type II (AN2) [MIM:106210]. AN2 is a bilateral panocular disorder characterized by complete or partial absence of the iris, absence of the fovea and malformations of the lens and anterior chamber. Severe age-related corneal degeneration is a frequent complication which contributes to a poor visual prognostis in aniridia. About one third of the cases are sporadic, and two thirds are familial, with autosomal dominant inheritance and high penetrance. Nearly one third of sporadic AN patients develop Wilms tumor in association with genitourinary anomalies and mental retardation (WAGR syndrome) as a consequence of heterozygous (sub)microscopic deletions of chromosome 11p13.,function:Transcription factor with important functions in the development of the eye, nose, central nervous system and pancreas. Required for the differentiation of pancreatic islet alpha cells (By similarity). Competes with PAX4 in binding to a common element in the glucagon, insulin and somatostatin promoters. Regulates specification of the ventral neuron subtypes by establishing the correct progenitor domains (By similarity). Isoform 5a appears to function as a molecular switch that specifies target genes.,similarity:Belongs to the paired homeobox family.,similarity:Contains 1 homeobox DNA-binding domain.,similarity:Contains 1 paired domain.,subunit:Interacts with MAF and MAFB.,tissue specificity:Fetal eye, brain, spinal cord and olfactory epithelium. Isoform 5a is less abundant than the PAX6 shorter form.,
  • 相關(guān)產(chǎn)品： RS0001,RS0002,YM3028,YM3029
  • 細(xì)胞定位： Nucleus .; [Isoform 1]: Nucleus .; [Isoform 5a]: Nucleus .
  • 組織表達(dá)： [Isoform 1]: Expressed in lymphoblasts. ; [Isoform 5a]: Weakly expressed in lymphoblasts.
  • 科研貨號(hào)： PLA004980
    • Hunan UPT Biotechnology Co.,Ltd
    Website：www.hyjdss.com Servive hotline :4006916686
    E-mail：service@uptbio.com
    Address：
    Room 402, Building 13, Xinggong International Industrial Park, 100 Guyuan Road, Yuelu District, Changsha City, Hunan Province, China.
普拉特澤實(shí)驗(yàn)室電話助手

4006916686

掃碼咨詢

精品人妻一区二区资源-欧美激情日韩激情亚洲最大-国产日韩欧美在线播放不卡-2019久久久高清日本道 | 五月婷婷丁香六月图片-超碰在线人妻观看-国产一区二区熟女综合-伊人久久大香线蕉av一区 | 精品人妻少妇一区二区三区四区-超碰国产原创在线观看-91中文字幕亚洲精品乱码在线-久久国产高清字幕中文 | 东京热视频中文字幕-热久久99热国产精品首页-国产亚洲精品女久久久久久久-成人精品在线免费观看视频 | 欧美激情综合在线三级-国产亚洲一区二区三区,-在线日韩av电影免费看-乱码人妻一区二区三区四区 | 久久综合婷婷国产二区高清-蜜桃精品一区三区-欧美午夜精品久久久久久8888-97超碰色偷偷 | 超碰在久久97-中文字幕 日韩三级-国产精品色哟哟在线免费观看-日韩欧美一区二区三区四区在线观看 | 精品日本加勒比一区二区三区-婷婷丁香六月中文字幕-蜜桃精品久久久久久-久久久久久久亚洲区婷婷 天天干天天躁久久综合-1024人妻一区二区三区-蜜桃久久久亚洲精品成-国产欧美日韩各 | 日韩未删减版电影-天天爽天天日天天摸-久久精品久久精品久-成人精品网站在线观看 | 精品视频精品人妻一区二区三区-激情久久综合精品久久-精品一区二区三区免费观看视频-久久99精品国产麻豆婷婷观看体验 | 久久精品国产亚洲情色-2020久久国产综合精品swag-日韩成人精品三级在线观看-国产欧美一区二区三区如水 | 久久精品我在看-国产又粗又长又硬又猛电影-日本一区中文字幕在线视频-日韩精品中文字幕在线观看网站大全 | 亚洲天堂中文字幕悠悠-久久夜久久久久-久久久久亚洲av毛片大全有-日韩欧美国产免费大片 | 日韩在线观看mm-欧美va天堂va视频va在线-91麻豆国产免费视频-91精品国产91久久久蜜臀 | 久久丝袜28p-婷婷久久网视频-天天舔天天摸天天碰-久久精品人人做人人爽电影蜜月 | 亚洲变态另类av一区二区三区四区-成人区人妻精品一区-97精品人妻一区二-欧美日韩国产一区片 | 麻豆精品一区二区观看-日韩午夜久久久久久久久久-亚洲天堂中文字幕网-日本精品一区二区三区不卡 色综合久久久久综合一小说-91福利视频下载-一本色道久久综合狠狠躁最新章节-999国产精品亚洲7777 | 国产av自拍第一页-蜜臂久久99精品久久久-久久中文字幕亚洲精品-欧美日韩亚洲在线观看视频 | 日韩av手机在线观看版-久久精品成人av蜜臀35p-精品久久久国产999-麻豆精品国产传 | 亚洲精品午夜久久久久久久久久-国产精品高潮呻吟av99-岛国av在线一区二区三区-日本一区二区三区四区在线 | 久久99久久com-欧美久久久久久久久久人妻-内射人妻日韩中文字幕在线观看-另类h中文字幕 | 国产成人av三级三级三级-久久婷婷综合激情-久久人妻天天av-伊人色婷婷在线 | 日本大黄高清不卡视频在线-久久香蕉av天堂第一-久久久久久久久久久久久久狠日-丰满少妇高潮一区二区三区 | 18禁国产精品久久久久久久久-亚洲制服丝袜人妻中文字幕-美日韩视频在线看-日韩午夜精选在线 | 丝袜日韩另类亚洲-婷婷激情深爱网-成人精品一区二区三区-91精品人妻人人做人人爽人人澡 | av中文字幕在线观看在线-久久久久精品国产乱码78m-国产麻豆剧传媒精品国产av吴梦-69中文字幕一区二区三区 | 欧美日韩在线视频第二页-国产又粗又黄又刺激视频免费-久久精品国产96精品亚洲九色-中文字幕在线人妻av | 国产精久久久久久精选-91精品人妻久久大师-精品人妻区一区二区三区在线视频-国产又大又黄又粗又猛 | 夜夜骚av.一区二区三区-日韩精品免费人成视频观看-免费精品日韩视频-色婷婷一二三区av | 久久精品视频3-国产亚洲一区二区三区在线观看-97国产一区二区三区-久久久久99久久久久 | 久久 中文字幕 亚洲-国产又粗又硬又爽又黄毛片-日韩中文字幕熟妇人妻在线-日韩四级片地址 | 久久久久久久免费看片-欧美,日韩不卡视频在线观看-中文字幕日本免费精品-无套内射区二区 | 久久综合久久在线观看-老鸭窝97久久久久精品-久久久国产一区二区三区四区小说-日韩久久精品日日骚懂色av | 精品国自产拍天天拍-国产91精品一二三-国产欧美日韩麻豆91-天天综合天天综合天天 | 中文字幕在线观看日韩av-亚洲欧洲日本色噜噜-日本久久这里有精品-久久综合久色综合 | 人妻少妇中文字幕三区-69精品久久久久久久久久久久-天天干天天操天天开心-久久超碰日韩精品 | 国产福利一区二区三区在线观看-妈妈的朋友4在线观看中文字幕-人妻精品二区三区更新-成人app免费看片 | 少妇高潮呻吟久久久久久av-av天堂中文官网-日韩一区二区三区四区在线观看-日韩电影免费一区二区 久久精品熟女俱乐部-国产一区二区三区福利-好好热在线观看视频-国产又粗又长又大又圆视频 | 精品人妻人妻人一区二区有限公司-精品午夜中文字幕熟女人妻在线-不卡视频一区二区免费看-69精品人妻久久久久久久久久久 | 精品人妻三区四区-97人妻一二区-日韩国产中文在线视频-国产精品久久自在自线不卡 | 国产成人一区二区三区欧美日韩成人-91婷婷久久激情-日日夜夜精品视频综合网-91精品国产91久久久久蜜臀 |